Complications of Evans' syndrome in an infant with hereditary spherocytosis: a case report View Full Text


Ontology type: schema:ScholarlyArticle      Open Access: True


Article Info

DATE

2009-09-10

AUTHORS

Hideki Yoshida, Hiroyuki Ishida, Takao Yoshihara, Takashi Oyamada, Masataka Kuwana, Toshihiko Imamura, Akira Morimoto

ABSTRACT

Hereditary spherocytosis (HS) is a genetic disorder of the red blood cell membrane clinically characterized by anemia, jaundice and splenomegaly. Evans' syndrome is a clinical syndrome characterized by autoimmune hemolytic anemia (AIHA) accompanied by immune thrombocytopenic purpura (ITP). It results from a malfunction of the immune system that produces multiple autoantibodies targeting at least red blood cells and platelets. HS and Evans' syndrome have different mechanisms of pathophysiology one another. We reported the quite rare case of an infant who had these diseases concurrently. Possible explanations of the unexpected complication are discussed. More... »

PAGES

40-40

References to SciGraph publications

Identifiers

URI

http://scigraph.springernature.com/pub.10.1186/1756-8722-2-40

DOI

http://dx.doi.org/10.1186/1756-8722-2-40

DIMENSIONS

https://app.dimensions.ai/details/publication/pub.1037058249

PUBMED

https://www.ncbi.nlm.nih.gov/pubmed/19740448


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