Successful plasma therapy in hemolytic uremic syndrome with factor H deficiency View Full Text


Ontology type: schema:ScholarlyArticle     


Article Info

DATE

2001-07

AUTHORS

Sylvie Nathanson, Véronique Frémeaux-Bacchi, G. Deschênes

ABSTRACT

A patient with homozygous factor H deficiency presented with hemolytic uremic syndrome (HUS) at the age of 7 months. After a 2-year period of stability, renal failure and erythrocyte fragmentation recurred between the age of 3 and 4 years. Fresh frozen plasma infusions allowed renal function to be improved and erythrocyte fragmentation to be stopped. Withdrawal of plasma therapy led to a relapse of the biological signs of HUS. More... »

PAGES

554-556

Identifiers

URI

http://scigraph.springernature.com/pub.10.1007/s004670100609

DOI

http://dx.doi.org/10.1007/s004670100609

DIMENSIONS

https://app.dimensions.ai/details/publication/pub.1038978190

PUBMED

https://www.ncbi.nlm.nih.gov/pubmed/11465803


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