Ontology type: schema:ScholarlyArticle
1970-06
AUTHORSJ. Amouroux, J. J. Bernier, J. C. Rambaud, A. M. Dupuy-Coin, S. R. Kalifat
ABSTRACTL'étude concerne la métastase ganglionnaire d'un carcinome médullaire de la thyroïde, évoluant depuis 9 ans, chez une jeune fille de 16 ans. Le tableau clinique était dominé par l'existence d'une diarrhée motrice et d'un flush syndrome. L'examen histologique a confirmé la structure particulière de cette tumeur à stroma amyloïde. La microscopie électronique montre des grains d'aspect neurosécrétoire dans le cytoplasme, et des fibrilles qui semblent être excrétées dans le milieu extracellulaire et participer à la formation de l'amyloïde. Il est généralement admis, depuis les travaux de Williams (1966) que ce carcinome dériverait des cellules C ou parafolliculaires, sécrétant la thyrocalcitonine. Cette activité sécrétoire ne rend pas compte des symptômes souvent associés, en particulier de la diarrhée; on peut suspecter l'association à la thyrocalcitonine de substances à activité vasopressive, telles que les kinines, la sérotonine ou la 5 hydroxytryptamine. More... »
PAGES122-130
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DOIhttp://dx.doi.org/10.1007/bf00525878
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