Ontology type: schema:Chapter
2013
AUTHORSJörg Fuchs , Verena Ellerkamp , Klaus-Peter Zimmer , Jens-Oliver Steiß , Almuthe C. Hauer , Stephan Buderus , Klaus-Michael Keller , Dietrich von Schweinitz , Florence Lacaille , Frank M. Rümmele , Olivier Goulet , Herbert Müller , Karl-Ludwig Waag , Claus Petersen , J. Fuchs , V. Ellerkamp , K.-P. Zimmer , J.-O. Steiß , A. C. Hauer , S. Buderus , K.-M. Keller , D. von Schweinitz , F. Lacaille , F. M. Rümmele , O. Goulet , H. Müller , K.-L. Waag , C. Petersen
ABSTRACTDuodenalatresien sind Hemmungsfehlbildungen und können proximal oder distal der Papilla Vateri entstehen, wobei die präpapillären Obstruktionen selten sind. Grundsätzlich kann zwischen einer Membranatresie und einer Defektatresie unterschieden werden. Die Unterscheidung beruht nicht nur auf embryologischen Gesichtspunkten, sondern hat auch eine klinische Bedeutung: Bei der Membranatresie kann die quergestellte, partiell offene oder geschlossene Membran weit in den distalen Duodenalanteil reichen („Windsackphänomen“), was zu diagnostischen und auch intraoperativen Problemen führen kann. Ein Pancreas anulare findet sich bei etwa 20 % aller Patienten mit Duodenalatresie. More... »
PAGES265-331
Pädiatrische Gastroenterologie, Hepatologie und Ernährung
ISBN
978-3-642-24709-5
978-3-642-24710-1
http://scigraph.springernature.com/pub.10.1007/978-3-642-24710-1_10
DOIhttp://dx.doi.org/10.1007/978-3-642-24710-1_10
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"description": "Duodenalatresien sind Hemmungsfehlbildungen und k\u00f6nnen proximal oder distal der Papilla Vateri entstehen, wobei die pr\u00e4papill\u00e4ren Obstruktionen selten sind. Grunds\u00e4tzlich kann zwischen einer Membranatresie und einer Defektatresie unterschieden werden. Die Unterscheidung beruht nicht nur auf embryologischen Gesichtspunkten, sondern hat auch eine klinische Bedeutung: Bei der Membranatresie kann die quergestellte, partiell offene oder geschlossene Membran weit in den distalen Duodenalanteil reichen (\u201eWindsackph\u00e4nomen\u201c), was zu diagnostischen und auch intraoperativen Problemen f\u00fchren kann. Ein Pancreas anulare findet sich bei etwa 20 % aller Patienten mit Duodenalatresie.",
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